Pulmonary function tests (maximum inspiratory pressure, maximum expiratory pressure, vital capacity, forced vital capacity) predict ventilator use in late-onset Pompe disease
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چکیده
منابع مشابه
Pulmonary function tests (maximum inspiratory pressure, maximum expiratory pressure, vital capacity, forced vital capacity) predict ventilator use in late-onset Pompe disease
In patients with Late-Onset Pompe Disease (LOPD), progressive respiratory muscle involvement leads to reduced pulmonary function, with respiratory failure the most common cause of mortality. Early disease manifestations include sleep-disordered breathing, which can be treated with non-invasive ventilation; however, progressive diurnal deficits can require invasive ventilation. To determine if p...
متن کاملResponse of Maximum Inspiratory Pressure and Functional Capacity to Positive End-Expiratory Pressure Device after Valvular Heart Surgery
Background: Pulmonary complications following valvular heart surgery are common and contribute to increased duration of hospital stay, rate of morbidity, and mortality. The purpose of the present study was to investigate the response of maximum inspiratory pressure and functional capacity to Positive End-Expiratory Pressure device in patients who underwent valvular hea...
متن کاملIn health--vital capacity is maximum in supine position.
Vital capacity, frequently measured clinically as an index of pulmonary function, gives useful information about the strength of respiratory muscles and other aspects of lung functions. It is generally noted in sitting position. As in the supine position, respiratory excursions of diaphragm is highest in normal breathing, this study was planned to note whether there occurred any alteration in v...
متن کاملIn search of maximum inspiratory and expiratory pressure reference equations.
Respiratory muscle weakness can occur in neuromuscular diseases as well as in pulmonary disease. For example, in chronic obstructive pulmonary disease, patients’ muscles may become weakened from hyperinflation, which causes the diaphragm to function at a poor mechanical advantage, or in patients on steroids that can result in myopathies. Pulmonary function tests are used to determine diagnosis,...
متن کاملSources of variation in forced expiratory volume in one second and forced vital capacity.
Published prediction equations for lung function differ considerably, but the components of population variation responsible for the differences are unknown. Data were analysed for 6,323 never-smoking adults who did not report wheeze or asthma, from 42 centres participating in the European Community Respiratory Health Survey. Means and components of variance were estimated for males and females...
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ژورنال
عنوان ژورنال: Neuromuscular Disorders
سال: 2016
ISSN: 0960-8966
DOI: 10.1016/j.nmd.2015.11.009